C12orf57

Clinical Characteristics

Mutations in C12orf57 may cause the following clinical manifestations:

Central Nervous System

  • Intellectual disability
  • Global developmental delay
  • Delayed gross motor development
  • Early-onset seizures (often intractable)
  • Absent speech
  • Delayed speech and language development
  • Generalized hypotonia
  • Spasticity
  • Hypertonia
  • Corpus callosum abnormalities
  • Thalamic hypoplasia
  • Abnormal septum pellucidum
  • Hypotonia
  • Hypertonia
  • Ventriculomegaly

Face

  • Micrognathia
  • Long face
  • Long philtrum
  • Frontal bossing
  • Low-set ears
  • Lop ears
  • Arched eyebrows
  • Beaked nose
  • Dental crowding
  • Microphthalmia
  • Iris, retina, choroid coloboma
  • Hypertelorism
  • Epicanthal folds
  • Upslanted or downslanted palpebral fissures

Skeletal

  • Brachydactyly of the toes and fingers
  • Bulbous thumbs
  • Talipes equinovarus
  • Pes planus
  • Genu valgum
  • Hip dislocation

Cardiovascular

  • Atrial septal defect
  • Ventricular septal defect
  • Pulmonic stenosis